DOI: 10.36347/sjams.2019.v07i03.013

Pages: 920-922

Ewing's soft tissue sarcoma is a rare condition that affects young adults. Primary neuroectodermal tumors (PNET) and soft tissue Ewing's sarcoma have long been considered as two distinct anatomo-clinical entities. More recently, it has been found that Ewing's sarcoma is only the most undifferentiated form of PNET. The diagnosis is essentially cytogenetics and immunohistochemistry. Given the absence of specific clinical and radiological signs, it seems necessary to include it in the differential diagnosis of any primary tumor of the soft tissues. The treatment is based on the combination of surgery, chemotherapy and radiotherapy. The high-dose multidrug therapy associated with hematopoietic stem cell transplantation significantly improves the long-term prognosis. We report, in this, work an observation of a patient who presents a Ewing sarcoma extra bone in the right leg.