DOI: 10.36347/sjmcr.2023.v11i02.004

Pages: 113-117

Introduction: Desmoplastic fibroma is a benign and rare intraosseous tumor. This lesion has local aggressiveness and a significant risk of recurrence. It can simulate a malignant tumor chart. Observation: A 11-year-old child who consulted for a mandibular swelling gradually evolving for 1 year. Swelling is associated with dental mobility without sensory disorders or cervical lymphadenopathy. Radiological signs are in favor with aggressive pathology. The biopsy revealed a desmoplastic fibroid or low-grade fibrosarcoma. Radical surgical treatment was performed. Discussion: This location is exceptional. No cases of mandibular localization have been reported in the literature. The clinical and radiological signs are not very specific. The diagnosis is most often pathological associated with histochemical immune. The recommended management is surgical by a wide resection.