DOI: 10.36347/sjmcr.2023.v11i02.006

Pages: 122-124

Adams-Oliver syndrome is a polymalformative disease rare whose incidence is estimated at 1/225,000. This is a female newborn, referred by the maternity ward on D0 of life, hospitalized for a polymalformative syndrome. We noted a shallow and non-traumatic parietal ulceration on a background of congenital aplasia of the scalp without bone defect, with peripheral venous ectasia, Cutis Marmorata, Congenital Telangiectatica. Moreover; second and third toe brachydactyly with nail agenesis. We managed the ulcerations with local care and offered regular follow-up to minimize the occurrence of serious complications. Unfortunately the newborn is lost to sight after a few days.