DOI: 10.36347/sajp.2023.v12i02.003

Pages: 44-47

Cordon, in the year 1767, was the first person to describe the extremely rare form of abnormality known as congenital aplasia of the skin. On the scalp, limbs, or abdomen, it manifests as a single, isolated lesion that affects multiple layers of skin and, on occasion, the bone. This is the most common form in which it presents itself. There has been some speculation that the condition could have a genetic component, a component related to the environment, or a component related to an exogenous factor. As of the end of 2013, there had been a total of approximately 500 cases reported from all over the world. The aim of the present study was to describe a rare case of ACC. An infant was diagnosed with ACC and a scalp lesion. The lesion was followed and described over one year.