DOI: 10.36347/sjams.2023.v11i02.017

Pages: 380-384

Behçet's disease is a vasculitis of the vessels affecting the arterial and venous territories whatever their calibers. It preferentially affects young subjects between 10 and 45 years old and also affects men and women. The history and physical examination are key steps in the diagnosis. We report the case of a 37-year-old patient with a history of repeated oral aphtosis for several months, chronic active smoker and former chronic alcoholic, in whom the revelation of Behçet's disease by the Budd-chiari syndrome, neuro-behçet and pulmonary embolism in the complication phase, this despite the multidisciplinary intervention, the vital prognosis was put into play. The revelation of Behçet's disease by multi-visceral complications justifies the diagnostic and management complexity, hence the importance of the contribution of imaging. These patients require early diagnosis of this polymorphic pathology and regular monitoring. Its manifestation by the Budd-Chiari syndrome is its seriousness due to its complications. Essentially all forms of liver disease are possible: fulminant, acute, subacute, chronic or an inaugural digestive hemorrhage by portal hypertension. The diagnostic delay in the complications phase, with multi-visceral involvement associating Budd-chiari syndrome, neuro-behçet and pulmonary embolism are the consequence of life-threatening.