DOI: 10.36347/sjmcr.2015.v03i10.019

Pages: 990-992

We present a case of Stargardt disease with unilateral good visual acuity in a 68-year-old man. His best corrected visual acuity was 0.9 in the right eye and 0.5 in the left eye. Fundus examination revealed atrophic macular area surrounded by numerous ill-defined grayish flecks in both eyes. Moreover, normal fundus coloration was maintained at the fovea in the right eye. Optical coherence tomography demonstrated irregular thickening of the retinal pigment epithelium, and the photoreceptor inner segment/outer segment (IS/OS) line was disrupted. However, IS/OS line was relatively preserved at the fovea in the right eye. Our findings may contribute to a better understanding of this rare condition.