DOI: 10.36347/sjmcr.2015.v03i12.015

Pages: 1192-1195

Defective enamel formation is the defects occurring at the stages of enamel formation. Amelogenesis imperfect (AI) is a hereditary disorder that causes developmental disturbances in the structure of enamel. Quantitative defects in matrix formation leads to hypoplastic form of Amelogenesis imperfecta. Inadequate mineralization of matrix leads to hypocalcification and hypomaturationvariants. It is very important to diagnose AI and provide functional and esthetic management of these patients to improve the oral health related quality of life.This paper describes a case of Amelogenesis imperfecta where both the father and son were affected with hypoplastictype.