DOI: 10.36347/sjmcr.2015.v03i12.017

Pages: 1199-1202

Extra nodal natural killer/T cell lymphoma of nasal type (Nasal NK/T cell lymphoma) is an uncommon type of extra nodal lymphoma. It is extremely rare in childhood. We present the case of a 16 year old boy with nasal NK/T cell lymphoma. He presented with an ulcerated lesion in the hard palate 3x2 cm, with slough and a perforation. A CT scan of the paranasal sinuses revealed an irregular enhancing lesion in the region of hard palate with erosion of the palatine process of both maxilla. Biopsy was diagnostic of NK/T cell lymphoma of nasal type, positive for CD7, CD3, CD56 and granzyme and plasma EBV DNA. PET scan showed FDG avid lesions in nasal cavity regions, peripancreatic region and cervical lymph nodes. He is undergoing chemotherapy with SMILE protocol and is planned for local XRT also.