DOI: 10.36347/sjmcr.2016.v04i07.030

Pages: 556-558

Atypical hemolytic uremic syndrome (aHUS) is an extremely rare, life-threatening, progressive disease that frequently has a genetic component. In most cases, it is caused by chronic, uncontrolled activation of the complement system, a part of the body’s immune system that destroys and removes foreign particles. About 33-40% of patients die or develop end-stage renal disease (ESRD) with the first clinical episode of aHUS even with the best supportive care. We report a case of atypical HUS with classical clinical & laboratory characteristics.