DOI: 10.36347/sjmcr.2016.v04i10.018

Pages: 760-764

We report a rare case of Maffucci’s syndrome in a 40 year old male patient presenting with dedifferentiated chondrosarcoma of right iliac bone developing from previous enchondroma along with multifocal enchondromas and haemangiomas involving various other bones predominantly on right side. In this case X-rays, CT scan and MRI were used to reach the final diagnosis. MRI was of aid to diagnose the dedifferentiated carcinoma even before the surgery. T2WI were used to distinguish between the dedifferentiated and the cartilaginous tumor. Furthermore, the dedifferentiated tumor had three elements-malignant fibrous histiocytoma, osteosarcoma and fibrosarcoma. This histological heterogeneity may be attributed to mesodermal dysplasia of Maffucci’s syndrome.