DOI: 10.36347/sjmcr.2016.v04i11.011

Pages: 842-844

Ochronotic arthropathy is a rare hereditary metabolic disease found in patients with alkaptonuria. It is associated with deposition of homogentisic acid derivatives in various connective tissues of the body. Joint involvement especially hip and knee destruction is seen. We present two cases of alkaptonuria resulting in ochronotic hip and knee arthritis treated with total hip and knee arthroplasties. Patients complaints were alleviated and no further complaints were registered, during the next follow-up.