DOI: 10.36347/sjmcr.2017.v05i02.019

Pages: 129-132

We present a long-term follow-up of a patient with Bietti crystalline dystrophy. The clinical findings were documented over a period of 4 years. The most striking features were crystalline deposits in the retina that were formed de novo with old ones replaced by chorioretinal atrophy. The visual fields were affected progressively during the course. Bietti crystalline retinopathy is a progressive retinal disease characterized by retinal crystals gradually replaced by atrophy of the retinal pigment epithelium and gradual constriction of visual fields. Our findings may contribute to a better understanding of the natural course of Bietti crystalline dystrophy.