DOI: 10.36347/sjmcr.2017.v05i05.013

Pages: 337-341

Rhabdomyosarcomas (RMS) are the malignant tumors of the striated skeletal muscles. RMS was first described by Weber in 1854 and accounts for 6% of all malignancies and represents 50% of all soft tissue sarcomas in children under 15 years of age. 1The most common sites of occurrence are the head and neck (40%), genitourinary tract (25%), and extremities (20%). 2Oral Rhabdomyosarcoma is rare neoplasm, and accounts for only 0.04% of all head and neck malignancies. 3 Even in the oral cavity when it occurs the most common site is soft palate.1 Here we present a case of 4 year old female child who was diagnosed as having rhabdomyosarcoma of the upper lip diagnosed by histopathology and confirmed by immunohistochemistry.