DOI: 10.36347/sjmcr.2017.v05i12.004

Pages: 823-826

Thrombotic thrombocytopenic purpura (TTP) is a rare thrombotic microangiopathy with an estimated incidence of 11 cases/million population per year. Early treatment is essential and is curative in this disease where lack of treatment results in 90% mortality. However, recognition of thrombotic thrombocytopenic purpura can be difficult because of the variety of presentations and lack of specific diagnostic criteria. We describe an atypical case of a patient with TTP who presented to our department for generalized swelling, and was found to have thrombocytopenia with anemia. Occasionally, an unusual clinical presentation makes TTP diagnosis difficult, thus resulting in a delay in the management of TTP. The current treatment is still plasmapheresis and application of steroids.