DOI: 10.36347/sjmcr.2018.v06i03.009

Pages: 147-148

Adult-onset Still Disease (AOSD) is a rare systemic inflammatory disease. Ocular involvement is exceptionally associated with Still’s disease. We present the case of a patient followed for AOSD who presented non-specific orbital inflammation involving the lacrimal gland. The diagnosis of dacryoadenitis was suspected after ruling out the other causes and the patient was treated with corticosteroids and methotrexate. Idiopathic orbital inflammation is rarely seen during AOSD. Recently, atypical ocular manifestations of AOSD have been reported. Biopsy indicated no signs of malignancy and ruled out sarcoidosis and vasculitis. Concerning infectious diseases, especially bacterial ones, a negative procalcitonin as well as the favorable response to corticosteroids allowed us to rule out their contingencies. This is an unusual presentation of an unusual disease.