DOI: 10.36347/sjmcr.2018.v06i11.009

Pages: 923-928

The juvenile granulosa tumors of the ovary are rare tumors, secreting estrogen, diagnosed by precocious puberty or a mass syndrome. Diagnosis is based on pelvic imaging: ultrasound and MRI, and hormonal balance sheet: estradiol, inhibin and Anti-Mullerian hormone. Their prognosis is quite favorable related to their diagnosis released at an early stage. We performed a retrospective descriptive study in the Visceral Pediatric Surgery Department "A" of children Rabat hospital, over a period of 18 years, during which 4 cases of juvenile granulosa tumors were listed. Our study focused on the analysis of the epidemiological profile, circumstances of discovery, clinical symptomatology, Para clinical characteristics and treatment started: The age of our patients was between 3 months and 14 years, precocious puberty and increased abdominal girth were the two main telltale signs. Pelvic ultrasonography was performed for all patients, the tumor was cystic in 2 cases and solido-cystic in 2 cases, an abdominal CT was performed in 3 patients and an MRI performed in one case, confirmed the ovarian origin of the abdominal pelvic mass. The hormonal balance achieved in two patients, revealed very low levels of gonad tropic hormones unlike the rate of estradiol which is very high income. Histological study micro follicular arrangement was predominant; the atypia was evident, with a positivity of all tumors vimentin, inhibin and CD99. The treatment was essentially surgical; all of our patients underwent unilateral oophorectomy by laparotomy. The evolution was marked by a case of postoperative recurrence, which underwent chemotherapy, adjuvant first, then palliative.