DOI: 10.36347/sjmcr.2018.v06i11.010

Pages: 929-933

We report a rare case of a primary cutaneus chordoma in a 12 years old girl. 12 years old girl, without a history, presented since two months a subcutaneous lesion of the neck, removed and whose histological study spoke of a chordoma, lost side for 3 months, with notion of a multinodular neck tumor quickly evaluating. Removal of the entire tumor with wide resection margins and radiotherapy doses, the histological result speaks for primary chordoma with absence of other locations after a radiological assessment. Chordoma is a rare, locally aggressive tumor that rarely causes metastasis, sitting exceptionally at the level of the skin primitively, it is a tumor of the adult, poses difficulties of surgical excision due to its locations, good prognosis in case of skin localization, in our patient and with respect for therapeutic modalities (surgery and radiotherapy) the prognosis in our patient was very reserved, she died a year later.