DOI: 10.36347/sjmcr.2019.v07i03.001

Pages: 172-174

Subependymal giant cell astrocytoma (SEGA) is a benign midline tumor of the central nervous system. It arises from the wall of the lateral ventricule and the foramen of Monro. It occurs in 10 to 15% of individuals with tuberous sclerosis complex (TSC), often before the second decade of age. These tumors have a slow evolutionary potential but may show aggressive local invasion with peri-lesional oedema and visual disturbances. The histological appearance is typical; It is a well-defined tumor, that morphologically associates astrocytic and ganglioneuronal elements. The double differentiation is confirmed by immunohistochemistry that shows cell expression of glial fibrillary acidic protein (GFAP) and vimentin. We report the case of a 9-year-old patient with isolated SEGA mimicking a sellar and suprasellar tumor with pituitary endocrine repercussions.