DOI: 10.36347/sjmcr.2019.v07i03.017

Pages: 226-230

Clouston syndrome is a form of ectodermal dysplasia that appears as a triad of clinical findings: palmoplantar keratoderma, nail dystrophy, and hypotrichosis. This study reports three cases of clouston syndrome: a father and his two children with universal hypotrichosis and onychodystrophy and normal sweating. The children lack hyperkeratosis and morphologic abnormalities of the teeth as originally described in Clouston syndrome. Management involves the use of special hair care products to help manage dry and sparse hair; wigs; artificial nails; and emollients to relieve palmoplantar hyperkeratosis.