DOI: 10.36347/sjmcr.2019.v07i04.001

Pages: 263-266

The Stewart-Treves syndrome is a rare and deadly entity, which is defined as cutaneous angiosarcoma arising in the setting of chronic lymphedema. It is typically a result of post-mastectomy lymphoedema, it also develops in Milroy disease, idiopathic, congenital, traumatic and filarial lymphoedema. It is extremely uncommon in the lower extremities as a result of idiopathic chronic lymphedema or secondary of radiotherapy for cervix cancer. The pathophysiology is poorly understood, and the treatment of Stewart-Treves syndrome is complex. Surgery remains the key to manage it. Unless the treatment, its prognosis is poor. We report a case of cutaneous angiosarcoma of the lower extremity in a patient with chronic lymphoedema secondary of radiotherapy and surgery for cervix cancer. The body scan didn’t show any metastatic lesions. The patient underwent acetabulum disarticulation with free margin, but she relapsed three months later. To the best of our knowledge, there are very few cases reported in the literature.