DOI: 10.36347/sjmcr.2019.v07i08.017

Pages: 517-519

Background: Botryoid rhabdomyosarcoma is a rare tumor of soft tissue. It arises almost in the vaginal or vesical wall and accounts for 3 to 4% of all cases of childhood cancer. Case report: we report a case of 36-months-old presented with bleeding and pelvic pain. Physical examination revealed a vaginal mass with grape-like feature protruding from the vagina. A biopsy was done and the anatomopathological exam revealed an embryonal botryoid type rhabdomyosarcoma. The staging workup including thoraco-abdomino-pelvic computed tomography scan and abdomino-pelvic magnetic resonance imaging didn’t show any metastatic lesion. The girl undergone neoadjuvant chemotherapy followed by conservative surgery and adjuvant external radiotherapy. Currently, the girl is disease-free with 5 years of regular follow up. Conclusion: the rarity of rhabdomyosarcoma in childhood leads to a lack of randomized controlled trials to guide the appropriate treatment. The new therapies conduct to increase the lifespan in those children. Actually, we tend to conservative treatments to preserve the quality of life.