DOI: 10.36347/SJMCR.2019.v07i10.004

Pages: 608-610

Cobb syndrome is an arteriovenous malformation defined by association of vascular cutaneous , muscular, osseous and medullary lesions at the same metamere or spinal segment.We report a case of 42-year-old woman who presented fifteen years ago an angiomatous cutaneous patch in abdominal and dorsal region associated with paraplegia and sphincter disorders. Clinical examination revealed a vegetal papulo-nodular angiomatous patch extending from the right hypochondrium to the dorsal region D10-D11.An abdominal angiography scan showed a thickening of the subcutaneous adipose tissue in band affecting the anterior, lateral and posterior abdominal wall. The medullary MRI has objectified a dorsal intramedullary process compatible with a lesion of vascular origin.The patient was referred for neurosurgery for management. Cobb syndrome is a rare arteriovenous malformation that can remain asymptomatic for a long time. Clinical follow-up and radiological exploration are necessary in any patient with metameric vascular lesions to prevent neurological deficit.