DOI: 10.36347/sjams.2023.v11i05.026

Pages: 964-963

Reporting a 37 year old male with pulmonary epithelioid hemangioendothelioma (PEH), whom had undergone a sleeve resection of main left bronchus en bloc with the tumour. Presented with shortness of breath & was treated as pneumonia with left lung collapse. Bronchoscopy showed lesion at left main bronchus & unable to pass the obstruction. CT scan showed left main bronchus endobronchial lesion & histopathological reported it as suspected PEH. Mass had regrown 90% stenosis within 2 weeks. PET scan showed solitary disease at left endobronchial region. Left thoracotomy with sleeve resection of left bronchus en bloc with the tumour done. Intraoperative bronchoscopy showed endobronchial tumour located at the main left bronchus 1cm from carina. Histopathology confirmed the resected lesions are PEH. Patient recovered well. PEH is a histological diagnosis, recent reviews showed that radiological CT findings can be associated. No standard guideline treatment for PEH. There are cases reported with good response to combine chemotherapy and immunotherapy. Unilateral lesions, surgery is indicated. If lesion is positive for oestrogen and progesterone receptors, studies showed that hormonal therapy may benefit. Antivascular endothelial growth factor reported as part of treatment. Prognosis is unpredictable. In view of the rarity of the disease, multi-modulated approach is essential in the management and follow-up of the patient.