DOI: 10.36347/sjmcr.2023.v11i06.007

Pages: 1064-1069

Summary: The objective of this publication is to report the case of a patient presenting an epithelioid angiosarcoma of the maxillary sinus with review of the literature in order to study the diagnostic, therapeutic and evolutionary aspects of this pathology. He is 60 years old. Active chronic smoker, who presented a painful swelling of the upper maxillary bone lateralized to the left. The radiological assessment described a lytic tumoral process at the expense of the floor of the maxillary sinus infiltrating the deep spaces of the face. A biopsy retained the diagnosis of a maxillary localization of an epithelioid angiosarcoma. Then, an extension assessment was able to eliminate the multifocal character and did not show any secondary localization. The patient subsequently underwent oncological surgery, with healthy excision limits. The evolution was favorable over a follow-up of one month. Angiosarcoma is a rare, high-grade malignant vascular tumour. For a third of the cases, these are multifocal tumours. There is a male predominance and a preferential location in the long bones and short bones of the extremities. They are observed at any age, with a median age of 51 years. In imaging, the radiological presentation is not specific but it is mainly to characterize the lesions and indicate their uni- or multifocality. Under microscopy, the most common angiosarcomas are epithelioid. One-piece surgical excision is the treatment of choice. They have an aggressive evolution with a 5-years survival rate between 10 and 30%. Adjuvant radiotherapy allows local control of 80% with good functional and cosmetic results. However, 50% of angiosarcomas develop metastases and irradiation does not improve survival.