DOI: 10.36347/sjmcr.2023.v11i06.046

Pages: 1219-1223

Dermatofibrosarcoma of Darier and Ferrand is a rare cutaneous tumor characterized by its local aggressiveness and high potential for recurrence. It rarely metastasizes, but when it does, the prognosis is poor. Surgery plays a crucial role in the management of these tumors, while targeted therapy is beneficial for metastatic or unresectable forms. Here, we present the case of a 50-year-old female patient who was admitted to our hospital for the management of metastatic dermatofibrosarcoma in the liver. The patient underwent wide excision surgery followed by treatment with imatinib. One-year follow-up showed a good response.