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Scholars Journal of Medical Case Reports | Volume-11 | Issue-10
Dyke-Davidoff-Masson Syndrome a Rare Cause of Cerebral Hemiatrophy: A Case Report
Chada Chbichib, Maryam El Khalifa, Imane Kazouini, Btissam Zouita, Dounia Basraoui, Hicham Jalal
Published: Oct. 22, 2023 | 114 78
DOI: 10.36347/sjmcr.2023.v11i10.034
Pages: 1854-1856
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Abstract
Cerebral hemiatrophy or Dyke-Davidoff-Masson syndrome (DDMS) is a rare clinical and radiological entity, characterized by seizures, facial asymmetry, contralateral hemiplegia or hemiparesis and mental retardation. These findings are due to a brain lesion that may occur early in life or in utero. Radiological features include unilateral loss of brain volume associated with compensatory bony alterations in the calvarium, such as thickening, hyperpneumatization of the paranasal sinuses and mastoid cells and elevation of the petrous crest. We report a case of a 13-year-old adolescent who presented with multiple episodes of generalized tonic-clonic seizures. In our case, the clinical history and CT imaging were sufficiently accurate to diagnose DDMS.