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Scholars Journal of Medical Case Reports | Volume-12 | Issue-02
Synovial Sarcomatous Transformation in Recklinghaussen Disease: A Case Report
Jihane Mhaili, Mohammed Boussif, Youssef Bouktib Ayoub El Hajjami, Badr Boutakioute, Meriem Ouali El Idrissi, Najat Cherif Idrissi El Ganouni
Published: Feb. 1, 2024 | 42 36
DOI: 10.36347/sjmcr.2024.v12i02.001
Pages: 129-132
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Abstract
Malignant sarcomatous transformation of neurofibromas MSTN are a major cause of mortality in patients with NF1, its optimal management and final prognosis depend on early and accurate detection. Through a case report and a literature review, we will discuss the specificity of sarcomatous transformation in Neurofibromatosis type 1.