DOI: 10.36347/sasjs.2024.v10i04.008

Pages: 438-441

Introduction: Most congenital ureteral strictures occur at the ureteropelvic or ureterovesical junction in children. Rare causes of hydronephrosis are congenital midureteral strictures. Definitive preoperative diagnosis is clinically challenging, and most patients are misdiagnosed preoperatively. Case presentation: We report 9 years old female child hydronephrosis. Renal scintigraphy with DTPA; revealed a normally functioning left kidney with split renal function of 47% and an obstructive pattern. Furthermore; Congenital Mid ureteric stricture is typically not diagnosed preoperatively, and definite diagnoses have been reached via retrograde assessment of the ureter; and surgical resection-anastomoses of the obstructed right ureteral tract allowed establishing normal ability of urine outflow. Conclusion: Pre-operative detection of Congenital Midureteric stricture is clinically challenging and requires a high level of attention. Whenever we observe a dilation of only the proximal segment of the ureter, we should keep this diagnosis in mind and discuss the images in detail with an experienced radiologist. The diagnosis should not be delayed in order to apply the appropriate approach surgery.