DOI: 10.36347/sjmcr.2024.v12i04.011

Pages: 422-426

Synovial sarcoma are extremely rare malignant tumors of soft extra-skeletal tissue accounting for less than 1% of all malignant tumors. Despite their name, they do not arise from synovial tissue, and their pathogenesis remains unknown. The knee and ankle are the most common sites of occurrence. Due to unclear risk factors, no screening recommendations currently exist. They are characterized by an unpredictable course; hence, multidisciplinary management must be initiated at an early stage in order to improve prognosis. The mainstay of treatment is wide surgical excision, which can often be challenging, requiring the sacrifice of noble structures, while reconstructive surgery can be laborious. The presence of pulmonary metastasis is an indication of poor prognosis. Herein, we report a rare case of a localized elbow synovial sarcoma in a 48-year-old woman with no comorbidity. She underwent surgery for complete tumor removal and had an uncomplicated post-operative follow-up.