DOI: 10.36347/sjmcr.2024.v12i05.020

Pages: 652-656

Ewing sarcoma (ES)/primary neuroectodermal tumor (PNET) is the second most common malignant bone tumor of childhood and adolescence. It can occur at central or peripheral sites, at skeletal or extraskeletal sites, and is more common at the femurs, ilium, and tibia. We report a rare case of Ewing's sarcoma of the scapula in a 2-year-old infant diagnosed with pain and swelling of the left shoulder. Histopathological confirmation of Ewing's sarcoma was possible following ultrasound-guided biopsy. Treatment consisted of initial chemotherapy, followed by surgical tumor resection after good initial response, followed by adjuvant therapy. The current post-treatment follow-up is 2 years without incident. This case is reported to highlight the rarity of localization and therapeutic modalities, particularly surgical.