DOI: 10.36347/sjmcr.2024.v12i07.013

Pages: 1261-1263

Desmoid tumors (DTs) are rare non-malignant tumors of mesenchymal origin. They are comprised of benign fibrous tissue with spindle-shaped cells adjacent to collagen. DTs may show aggressive fibroblastic proliferation. They do not metastasize, but may exert local infiltration with a recurrence tendency. DTs are classified into superficial or deep ones. Moreover, they can be of sporadic or familial types. Aggressive fibromatosis usually occurs in the deep soft tissues. It is characterized by proliferation of fibrous tissue and infiltration of the adjacent structures. The clinical management of DTs is very complex and requires a multidisciplinary approach. We present here a 8-year-old male child with chest wall aggressive fibromatosis, who was treated with surgery followed by adjuvant radiation therapy. The patient is doing well following 12 months of follow-up without local recurrence. Radical surgical resection is the main treatment for DTs. The adjuvant treatment, either chemotherapy or radiotherapy, can be considered when radical resection could not be achieved and if reoperation for a recurrence is not applicable. Close follow-up is essential in such patients.