DOI: 10.36347/sasjs.2024.v10i07.022

Pages: 844-850

Darier-Ferrand dermatofibrosarcoma is a rare skin tumor, generally diagnosed late, given its character, its slow and painless evolution as well as its lack of awareness by practitioners. After histological confirmation, treatment is planned according to the location and extent of the lesions in order to predict possible aesthetic and functional sequelae. Surgical resection and the gold standard. It is because of the high recurrence rate associated with wide local excision, the introduction of Mohs micrographic surgery, when the technical platform is suitable, has really helped to reduce recurrence rates dermatofibrosarcoma. But skin reconstruction, after significant loss of substance secondary to a resection respecting safety margins, represents a surgical challenge. Imatinib is recommended for neoadjuvant treatment to reduce tumor mass as well as in cases of unresectable or metastatic tumors. radiotherapy can be offered after incomplete surgery without any benefit after complete resection. In this paper we report the case of a patient operated for extensive lesions of the subumbilical wall in favor of a Darier-Ferrand dermatofibrosarcoma whose management of the loss of substance was a surgical challenge.