DOI: https://doi.org/10.36347/sjmcr.2024.v12i10.023

Pages: 1715-1719

Unilateral pulmonary artery hypoplasia is a rare congenital malformation. The diagnosis is usually set at adolescence, however it can remain asymptomatic and late diagnosis is possible. Radiologically, this anomaly may be suggested on a standard chest X-ray but must be confirmed by angiography. We report the case of a young patient, 51 years old, presenting with NYHA stage II dyspnea. An angiogram was performed and revealed hypoplasia of the right pulmonary artery. The management of these patients is not yet consensual and depends on clinical evolution. However, it most often consists of regular clinical and paraclinical monitoring to detect potential complications.