DOI: https://doi.org/10.36347/sjmcr.2025.v13i02.009

Pages: 254-257

Echinococcosis is endemic in Mediterranean countries, with the lungs and liver being the most affected organs in childrens. Primary biliary tract hydatid cyst is an exceptional localization. A 4-year-old child was referred to our surgical outpatient department due to suspicion of a DKC, based on right upper quadrant abdominal pain accompanied by jaundice. Physical examination revealed mild tenderness in the right upper quadrant of the abdomen. An ultrasound complited with an MRI described a Todani type 4 choledochal cyst. The patient underwent right subcostal laparotomy, during which exploration revealed a cystic formation of the choledochus from which clear fluid was aspirated. Upon opening the cyst, a proligere membrane was found, confirming the diagnosis of choledochal hydatid cyst. Primary hydatid cyst of the bile ducts is an extremely rare entity, which is why radiologists do not consider this diagnosis to be primary.