DOI: https://doi.org/10.36347/sjmcr.2025.v13i05.115

Pages: 1210-1212

Primary pulmonary sarcomas are extremely rare malignant tumors of mesenchymal origin, representing less than 0.5% of all primary lung malignancies. Due to their rarity and non-specific clinical and radiologic features, diagnosis is often delayed. We report the case of a 26-year-old patient presenting with a primary undifferentiated pulmonary sarcoma of FNCLCC grade II. Diagnosis was established through imaging and histopathological examination. Despite initiation of chemotherapy, the disease progressed rapidly and the patient died shortly after the third cycle. We discuss the diagnostic challenges and therapeutic considerations in managing such rare and aggressive tumors.