DOI: https://doi.org/10.36347/sjmcr.2025.v13i06.008

Pages: 1335-1338

Moya Moya disease (MMM) is a chronic cerebral arteriopathy of undetermined etiology, characterized by steno-occlusive lesions of the terminus of the intracranial internal carotid arteries and the proximal part of the arteries of the polygon of Willis, with development of a fine anomalous compensatory vascular network. It affects both children and young adults, and is a frequent cause of stroke in children. Imaging plays a fundamental role in diagnosis, therapeutic strategy and follow-up. Non-invasive, non-irradiating MRI plays a fundamental role in monitoring this disease. The prognosis for MMM is guarded: in the absence of treatment, symptoms worsen and the risk of stroke increases. Surgical revascularization techniques appear to improve cerebral perfusion. We report the case of two children with Moya-Moya disease.