DOI: https://doi.org/10.36347/sjmcr.2025.v13i06.048

Pages: 1498-1501

Bone fibrous dysplasia (BFD) is a rare, congenital, sporadic disease of benign bone involvement responsible for bone deformity involving defects in osteoblast dedifferentiation, medullary fiber proliferation and osteoclast hyperactivity. There are two forms of the disease: monostotic, with single lesions, and polysostotic, with multiple lesions. Sarcomatous evolution is exceptional. It may be encountered in syndromic conditions, such as MacCune Albright syndrome, which associates DFO with endocrine disorders and café-au-lait stains; Mazabraud syndrome, corresponding to the association between intramuscular myxoma and DFO. We report a case of DFO collected in the radiology department on August 20, 1953.