DOI: https://doi.org/10.36347/sjmcr.2025.v13i08.012

Pages: 1805-1807

The coexistence of renal agenesis with contralateral renal ectopia is extremely rare: to date, no similar case has been reported in the literature. The ectopic kidney may show dilation of the collecting system. We report here the case of a 17-year-old patient with a dilated and destroyed pelvic ectopic right kidney (hydronephrosis due to ureteropelvic junction obstruction) associated with contralateral renal agenesis, discovered incidentally on ultrasound. Initial management involved close monitoring, but progression to end-stage renal disease due to the destruction of the solitary kidney led to definitive treatment with laparoscopic right nephrectomy. The patient was placed on peritoneal dialysis. Surgical exploration revealed a right renal artery originating from the anterior surface of the terminal aorta.