DOI: https://doi.org/10.36347/sjmcr.2025.v13i10.003

Pages: 2193-2194

Schizencephaly and Dandy-Walker syndrome are two rare congenital malformations of the central nervous system, distinguished by their location and characteristics. Complex developmental processes involving both the cerebral cortex and the cerebellum are thought to contribute to this anomaly. We report the case of a 3-year-old girl, who underwent surgery two years earlier for hydrocephalus with the placement of a ventriculoperitoneal shunt, and has a history of epilepsy. In this context, she underwent a brain CT scan for etiological purposes, which revealed schizencephaly associated with Dandy-Walker malformation.