DOI: https://doi.org/10.36347/sjmcr.2025.v13i10.014

Pages: 2242-2246

Pseudoxanthoma elasticum (PXE) is a systemic disorder often revealed by angioid streaks (AS), whose main vision-threatening complication is choroidal neovascularization (CNV). We report the case of a 42-year-old patient presenting with decreased visual acuity and metamorphopsia in the right eye. Fundus examination showed bilateral AS with a “peau d’orange” pattern, and OCT confirmed CNV with subretinal fibrosis. Despite intravitreal anti-VEGF therapy leading to partial anatomical improvement, visual function remained limited. This case highlights the importance of early detection and prompt treatment of PXE-related CNV to preserve vision.