DOI: https://doi.org/10.36347/sjmcr.2026.v14i06.019

Pages: 1400-1402

Lhermitte-Duclos disease, also known as dysplastic cerebellar gangliocytoma, is a rare and benign tumor of the central nervous system. It is characterized by a hypertrophic ganglionic proliferation, which preferentially affects the cerebellar cortex, with an abnormal laminar arrangement [1]. Magnetic resonance imaging plays a major role in identifying this pathology. We report a case of a patient monitored for Cowden syndrome who presented with left hemiparesis and balance disorders. Brain MRI demonstrated a left hemispheric area, poorly defined, with isointense signal on T1 and hyperintense signal on T2 and FLAIR, and diffusion without ADC restriction, not enhanced after Gadolinium injection. This area is crossed by hypointense striations creating a striated and lamellar appearance. We shed light through this clinical case of a known Cowden syndrome carrier on the radiological aspects of this rare entity.