DOI: https://doi.org/10.36347/sasjs.2026.v12i07.004

Pages: 600-605

Nasal gliomas or heterotopias are rare, nonhereditary, congenital midline or paramedian tumors composed of heterotopic neuroglial tissue. We report the case of a 2-year-old boy with a right later nasal swelling present since birth, associated at birth with an anterior skull-base meningo-encephalocele with right naso-orbital development for which he underwent neurosurgical repair at the age of 6 months. He was subsequently referred to the maxillofacial surgery department at the age of 2 years for management of the residual nasal mass. Imagery revealed a well-defined ovoid right paranasal soft-tissue process compressing the frontal process of the maxilla without bone lysis and respecting the homolateral orbit, together with a persistent and widened front-nasal suture, and no abnormal cerebral parenchymal enhancement. Complete surgical excision was performed through an external later nasal cutaneous approach. Histopathological examination confirmed the presence of a nasal glial heterotopia without signs of malignancy. The postoperative course was uneventful, with no recurrence. This report reviews the clinical, radiological, and histological features of this rare malformation, together with the main embryopathogenic hypotheses discussed in the literature.