DOI: https://doi.org/10.36347/sjmcr.2026.v14i07.012

Pages: 1658-1661

Background: Congenital adrenal hyperplasia (CAH) is most common cause of virilization and clitoromegaly in genetically female children. Excess androgen production during fetal life may result in enlargement of the clitoris, sometimes resembling a penile structure. CAH due to 21-hydroxylase deficiency accounts for most cases of genital ambiguity in 46 females. [1,2] We report a case of 3-year-old female child, previously diagnosed with congenital adrenal hyperplasia, presented with clitoromegaly. Clinically, the enlarged clitoris resembled a small penis. Surgical reduction clitoroplasty was performed. Histopathological examination of the excised specimen showed benign hypertrophy of clitoral tissue. No evidence of malignancy, dysplasia, or neoplastic lesion was identified. Conclusion: Clitoromegaly in children is most commonly associated with congenital adrenal hyperplasia. Histopathological examination confirms the diagnosis by demonstrating normal clitoral erectile tissue with hypertrophy secondary to androgen exposure. Early diagnosis and multidisciplinary management are important for optimal functional and cosmetic outcomes.