DOI: 10.36347/sjmcr.2020.v08i12.003

Pages: 994-999

Objective: Describe the different therapeutic modalities of Branchio-oto-renal (BOR) Syndrome. Material and method: We report the case of a 7-year-old boy who presented with a Branchio-oto-renal syndrome (BOR). Clinical Case: T.S, a 7-year-old child presented from the age of 3 years, a progressive, bilateral deafness, with a preserved language. The otological examination found implanted low ears, bilateral prehelic fistulas, and left seromucosal otitis CT scan showed bilateral vestibulo-labyrinthine malformation confirmed by the MRI. Cochlear implant surgery on the right ear was performed. Conclusion: The therapeutic principle is based on the precociousness of the rehabilitation of a quality auditory canal, which remains a factor of good prognosis of bilateral deafness of the child reached of the syndrome of BOR. A quality ear canal is defined by an ability to perceive and understand speech by the ear canal alone. Severe or deep bilateral deafness is the subject of hearing rehabilitation by hearing aid or cochlear implant, speech therapy and educational support.