DOI: 10.36347/sjmcr.2020.v08i12.010

Pages: 1023-1028

Background: Congenital cervical dysgenesis with or without vaginal agenesis is a rare Müllerian developmental disorder that occurs in one in every 80,000 to 100,000 births. Cervical abnormalities two basic anatomical types. First, the cervix is absent with narrow lower uterine segment and absent vagina cervico vaginal agenesis. The second type is cervical dysgenesis. Management options for such conditions include total abdominal hysterectomy or conservative surgery with uterovaginal anastomosis, cervical canalization, or cervical reconstruction. In our case report, the patient had cervico vaginal dysgenesis. Objective: Aim is to successful reproductive out come after reconstructive surgery of cervicovaginal dysgenesis. Case report: Mrs. Rabeya came to BSMMU on 08/11/08 with primary amenorrhea with hematometra with vaginal agenesis at 15 yrs old. Reconstruction of cervix & vaginoplasty done & menstruation started. Upto 7 years after 1st operation her menstrual cycle was regular but scanty flows with severe dysmenorrhea. Above these complaint’s she again came to BSMMU at 2015 and reconstruction surgery was done due to narrowness of cervico vaginal space at that time. After 2nd operation her menstrual flow was average & dysmenorrhea decreased. She got married at 2017. Four months after her marriage she developed severe dyspareunia & came to BSMMU & admitted on 10/08/17. Re-anastomosis of cervico vaginal stenosis and resection of septum done for 3rd time and cervico vaginal canal restored. Her dyspareunia was improved. Now after her 3rd time operation she enjoying her new life & spontaneous pregnancy occur. Finally LUCS was done at her 36wks pregnancy on 6th May 2019. Discussion: A total of approximately 200 cases of congenital cervical atresia have been reported in the literature. The experience from reconstructive uterovaginal anastomosis was not satisfactory. Rock et al., recently reviewed 30 cases of cervical agenesis and dysgenesis that underwent reconstructive....