DOI: 10.36347/sjmcr.2021.v09i01.013

Pages: 48-50

Jejunoileal atresia (JIA) and stenosis are the most common congenital anomalies of the small intestine and are a major cause of intestinal obstruction in neonates. The traditional classification of JIA proposed by Grosfeld included 4 subtypes of which type IIIB, or apple-peel atresia, is characterized by a proximal atretic jejunum and a distal segment of spiralled bowel that terminates at the cecum. These patients are at increased risk for short bowel syndrome and subsequent intestinal failure. We hereby describe a case of a neonate with JIA who was initially found to have a type IIIB atresia but there was a variation as she had a length of normal small bowel and mesentery proximal to cecum attached distal to spiralled segment of bowel. Surgical correction proceeded with minimal resection and primary anastomosis. She recovered well from this procedure, tolerated full enteral nutrition by mouth, and displayed good weight gain at outpatient follow-up. Due to the unique anatomy of the gastrointestinal tract in this case report, we propose the addition of a new class of JIA, type IIIC, to better reflect its prognostication and surgical management.