DOI: 10.36347/sjmcr.2021.v09i01.020

Pages: 74-76

Background: Epithelioid sarcoma is a rare malignancy that presents diagnostic difficulties. Case: A 22 years old female presented with epigastric pain, vomiting and haematemsis. Admitted for resuscitation and management , workup showed multiple duodenal and pancreatic hemangioma’s underwent laprotomy end up with whipple’s procedure, unfortunately she develop post op convulsion’s , discovered to be due to brain metastasis , she passed away, histopathology came as epitheloid sarcoma. A review of different cases of similar condition is provided. Conclusion: The diagnosis of epithelioid sarcoma needs a high index of clinical suspicion and immunohistochemistry. Prognosis is determined by adequacy of the initial surgical procedure and early detection plays a major role and important predictor of recurrence.