DOI: 10.36347/sjmcr.2021.v09i02.016

Pages: 178-180

Melorheostosis is a rare bone disorder that could be associated with soft tissue anomalies and result in chronic pain, joint deformities, and significant esthetic impact. Melorheostosis has been reported to be associated with a broad spectrum of skin changes, including scleroderma. However, systemic disorders and particularly chronic rheumatic diseases are not a common association. We report the case of a 53-years-old female patient with unknown co-morbidities who presented with the unusual association of diffuse melorheostosis, linear scleroderma, and primary Sjögren syndrome resulting in severe joint deformities. The patient was treated with radical orthopedic surgery.