DOI: 10.36347/sasjs.2021.v07i03.007

Pages: 137-140

Angiosarcoma is a rare neoplasm typically presenting in the skin and superficial soft tissues which comprise less than 2% of all sarcomas and are aggressive in nature. They often present with a bruise-like appearance which can progress to nodular and ulcerated lesions. While angiosarcoma can arise anywhere in the body, they rarely occur in the female genital tract. This case report of a 40 years old post menopausal women attending the Gynae OPD of Assam Medical College with a swelling in the left side of the vulva for last 2 years which was progressively increasing in size. It was painless causing discomfort while walking. There was no history of discolouration of skin, prior radiation therapy, family history, difficulty in micturition or any discharge per vaginum. Her bowel habit was normal. Her general condition was fair and vitals were stable. Local examination revealed a (10 × 10 x 4) cm lump extending from the mons pubis to the left labia majora without inflammatory signs or discharge. Clitoris and rest of the vulva was normal but the urethral meatus was deviated to the right side. Examination of the vagina revealed a left sided large swelling with normal introitus and pelvis was normal and there was no inguinal lymphadenopathy. The patient was planned for surgery and enucleation was done. Histopathology revealed it to be an epithelioid vulvar angiosarcoma. The literature supports surgical excision as the primary treatment of choice for angiosarcoma, although the prognosis remains poor even with early intervention whereas loco- regional and systemic chemotherapy have shown little success in improving survival. Given the overall poor prognosis of angiosarcoma, early detection remains the key element in maximizing patient outcome.