DOI: 10.36347/sjmcr.2021.v09i04.011

Pages: 349-351

A 62-year-old man was referred to our clinic for an ocular fundus abnormality discovered during a medical checkup. He had no subjective complaints. Ophthalmoscopic examinations of the fundi did not reveal any abnormalities in the left eye. In the right eye, a round to oval area of hypopigmentation was seen in the macula, and normal fundus coloration was maintained in the fovea of the right eye. Fundus autofluorescence showed hypoautofluorescence corresponding to the area of hypopigmentation. Optical coherence tomography demonstrated disruption of the ellipsoid zone (EZ) corresponding to the area of hypopigmentation. However, the EZ was relatively preserved in the fovea of the right eye. Based on these collective findings, we diagnosed our patient with unilateral central areolar choroidal dystrophy (CACD). CACD is commonly observed in both eyes. Our findings may contribute to a better understanding of this rare condition.